Primitive Neuroectodermal Tumors

These tumors arise from primitive nerve cells in the central nervous system, and they are quite rare. Primitive Neuroectodermal Tumors are more common in children, and they are highly malignant. There are at least three subtypes depending on the tissue of origin, and altogether they account for 4 to 17% of soft tissue tumors in children. In the central nervous system, they cause symptoms depending on their location.